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5 Facts you should know about

Churg-Strauss syndrome (2)

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1

A condition characterized by asthma, high levels of eosinophils, and inflammation of small to medium blood vessels (vasculitis)

2

The inflamed vessels can affect various organ systems including the lungs, gastrointestinal tract, skin, heart, and nervous system

3

Also called eosinophilic granulomatosis with polyangiitis (EGPA), it is considered to have three distinct phases - prodromal (allergic), eosinophilic, and vasculitic - which don't always occur sequentially. (Some people do not develop all 3 phases)

4

The disease was first described in 1951 by Dr. Jacob Churg and Dr. Lotte Strauss as a syndrome consisting of “asthma, eosinophilia (an excessive number of eosinophils in the blood), fever, and accompanying vasculitis of various organ systems"

5

The typical patient with EGPA is a middle-aged individual with a history of new-onset or newly worsened asthma

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