Rare Medical News

5 Facts you should know about

DOCK8 deficiency

fivefacts-light.svg

1

It is the autosomal recessive form of hyperimmunoglobulin E syndrome.

2

The signs and symptoms of DOCK8 deficiency are similar to the autosomal dominant form, STAT3 deficiency.

3

DOCK8 deficient children often have eczema, respiratory and skin staphylococcus infections.

4

The low number of T cells (T cell lymphopenia) and other lymphocytes appears to be responsible for the susceptibility to infections, and the poor humoral immunity is responsible for low response to vaccines.

5

Children with DOCK8 deficiency do not tend to live long; sepsis is a common cause of death at a young age.

Rare Medical News